Gastroenterologie
a hepatologie

A rare cause of increased abdominal size

Karel Dvořák ^{Orcid.org  1}, Jan Fulík²

+ Affiliation
¹ Oddělení gastroenterologie a hepatologie, Krajská nemocnice Liberec, a.s., Nemocnice Liberec
² Chirurgická klinika 1. LF UK a IPVZ Nemocnice Na Bulovce, Praha

Summary

We present a patient with an increased abdominal size and epigastric pain. Pseudomyxoma peritonei was diagnosed based on imaging studies. This is a rare clinical condition characterized by diffuse gelatinous collections in the abdomen and pelvis that are associated with mucinous implants on surfaces in the peritoneal cavity. It is caused by cystadenoma of the appendix, which leads to peritoneal seeding of mucus-producing cells. Mucins fill the peritoneal cavity. This condition has an indolent but progressive course and is fatal if untreated. The treatment of choice is radical surgical cytoreduction and heated intraperitoneal chemotherapy, which may have curative  potential.

Keywords

HIPEC, cystadenoma of the appendix, cytoreduction, pseudomyxoma peritonei

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