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Gastroenterologie
a hepatologie

Gastroenterology and Hepatology

Gastroent Hepatol 2022; 76(1): 67–71. doi: 10.48095/ccgh202267.

Desmoid fibromatosis – a rare mesenteric tumor

Lukáš Grochol1, Ivana Cibulková1, Jan Hrudka2, Jan Hajer Orcid.org  1

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Summary

In the following report, we present the case of a 31-year-old patient examined for a suspected small bowel tumour. Small bowel tumours are relatively rare and definitive diagnosis is often preceded by surgical resection. The same was true for our patient examined for a soft tissue lesion found with imaging techniques in close proximity to the small intestine. After ruling out hormonal activity, diagnostic laparotomy was performed. Desmoid fibromatosis, a rare tumour of the mesentery, was confirmed histopathologically. Although without metastatic potential, desmoid fibromatosis is a tumour with moderately malignant potential for aggressive growth into surrounding structures and organs and a large percentage of local recurrences.

Keywords

mezenterium, esmoidní fibromatóza, nádory tenkého střeva

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